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Involvement of spinal nerves in neurofibromatosis

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Abstract

Spinal tumors are a frequent form of manifestation of neurofibromatosis. Out of 171 patients, who have been operated on over a ten years period on spinal tumors, 7 patients had neurofibromatosis (4.1%). A total of 9 operations were performed, removing 20 spinal tumors. Three patients had multiple neurofibromas. Half of the neurofibromas had a dumbbell configuration with a larger extraspinal extension. In three patients a family history of neurofibromatosis and typical dermatological signs were evident. Two cases will be selected and the basic concept regarding treatment and the risks involved will be discussed.

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Tatagiba, M., Bini, W., Sepehrnia, A. et al. Involvement of spinal nerves in neurofibromatosis. Neurosurg. Rev. 17, 43–49 (1994). https://doi.org/10.1007/BF00309986

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