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Michel dysplasia

Common cavity inner ear deformity

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Abstract

A case is reported in whom there was a unilateral complete arrest of differentiation of the otocyst associated with an ipsilateral mild hemifacial hypoplasia and auricular abnormalities. The patient’s tympanic membrane and VII nerve function were normal and a normal ossicular mass was identified on CT Scan. This case illustrates that development of the middle ear cavity (exclusive of structures on the medial wall), external ear canal and VII nerve can be independent of development of the inner ear and that a unilateral absence of otic capsule differentiation can take place without severe associated abnormalities.

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References

  1. Jensen J (1969) Malformations of the inner ear in deaf children. Acta Radiol [Suppl] 286: 1

    Google Scholar 

  2. Schuknecht HF (1967) Pathology of sensori neural deafness of genetic origin. In: McConell F, Word PH (eds) Deafness in childhood. Vanderbilt University Press, Nashville, pp. 69–90

    Google Scholar 

  3. Jackler RK, Luxford WM, House WF (1987) Congenital malformations of the inner ear. A classification based on embryogenesis. Laryngoscope [Suppl 40] 97: 2

    PubMed  CAS  Google Scholar 

  4. Lindsay JR (1973) Profound childhood deafness. Ann Otol Rhinol Larnygol [Suppl 1] 82: 4

    Google Scholar 

  5. Van De Water TR, PcPhee JR (1987) Determinants of otic capsule formation. Laryngoscope 97: 315

    PubMed  Google Scholar 

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Kavanagh, K.T., Magill, H.L. Michel dysplasia. Pediatr Radiol 19, 343–345 (1989). https://doi.org/10.1007/BF02467313

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  • DOI: https://doi.org/10.1007/BF02467313

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