Cutaneous angiosarcoma arising in the radiation site of a congenital hemangioma

doi:10.1016/0190-9622(95)90424-7

Journal of the American Academy of Dermatology

Volume 33, Issue 5, Part 2, November 1995, Pages 865-870

https://doi.org/10.1016/0190-9622(95)90424-7 Get rights and content

Abstract

We describe a patient in whom angiosarcoma developed at the site of a hemangioma that was treated during infancy with radiation for refractory thrombocytopenia. Our findings, along with those of the 10 reported cases from the world literature, are summarized. One third of angiosarcomas arise in the skin. They most often show one of three clinical patterns. First and most common is occurrence as a bruiselike lesion on the scalp or face of an elderly person. Second in frequency is the Stewart-Treves syndrome. Third and least common is angiosarcoma developing as a sequela of previous radiation therapy. The prognosis in general is poor, with a mean survival length of 24 months and a 5-year survival rate of 10%. Effective treatment relies on early diagnosis and wide-margin surgical excision.

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^☆: The opinions or assertions contained herein are the private views of the authors and are not to be construed as official or as reflecting the views of the U.S. Army or the Department of Defense.

^☆☆: Reprints not available from authors.

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Case reportCutaneous angiosarcoma arising in the radiation site of a congenital hemangioma☆,☆☆

Abstract

J Maxillofac Surg

Pathol Res Pract

Am J Surg

Med Clin North Am

J Am Acad Dermatol

Chest

Dermatol Clin

J Am Acad Dermatol

J Am Acad Dermatol

Am J Surg

Malignant blood vessel tumors: a report of 56 cases of angiosarcoma and Kaposi's sarcoma

Surg Gynecol Obstet

Angiosarcoma of the temporal region following roentgen therapy of hemangioma of the cheek

Med Radiol

Hemangiosarcoma subsequent to radiotherapy for a hemangioma in infancy

J Dermatol Surg Oncol

Radiation-induced soft-tissue and bone sarcoma

Radiology

Angiosarcoma arising in an angiomatous naevus following irradiation in childhood

Br J Dermatol

Juvenile cutaneous angiosarcoma following radiotherapy of a hemangioma

Pathologica

Postirradiation malignant transformation in benign haemangioma

Eur J Surg Oncol

Malignant vascular tumors

Angiosarcomas of the skin

Semin Diagn Pathol

Tumors of vascular tissue

Angiosarcoma of the face and scalp, prognosis and treatment

Cancer

Lymphangiosarcoma in postmastectomy lymphedema: a report of six cases in elephantiasis chirurgica

Cancer

Lymphangiosarcoma arising in chronic lymphedematous extremities

Cancer

Lymphangiosarcoma

Cancer

Lymphangiosarcoma of a congenitally lymphedematous arm

Arch Pathol

Case report
Cutaneous angiosarcoma arising in the radiation site of a congenital hemangioma☆,☆☆