Elsevier

The Journal of Pediatrics

Volume 85, Issue 3, September 1974, Pages 345-349
The Journal of Pediatrics

Original article
Extending the scope of the VATER association: Definition of the VATER syndrome

https://doi.org/10.1016/S0022-3476(74)80113-7Get rights and content

Analysis of malformations in 10 new cases of the VATER association as originally defined by Quan and Smith 1a,band in 24 previously reported cases showed that two other anomalies, namely ventricular septal defect (VSD) and single umbilical artery (SUA), occurred frequently. It is suggested that the scope of the VATER association be enlarged to include these malformations and thus the V in VATER would stand not only for vertebral defects but also for vascular anomalies including VSD and SUA.

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    Supported by a grant from the National Foundation-March of Dimes.

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