Case reportMalignant mesenchymal tumor arising from cherubism: a case report
Section snippets
Report of a case
A 10-year-old boy was seen for diagnosis and treatment of swelling of the entire face that had been gradually increasing since the age of 3 years. The child’s parents were concerned about his appearance and desired cosmetic improvement and arrest of the facial growth.
Physical examination revealed increase in both horizontal and vertical dimensions of the lower two thirds of the face (Fig 1). The skin over the expanded jaws was stretched so thin that underlying blood vessels were visible on the
Discussion
Cherubism is a benign, hereditary bone condition of the jaws. Its histopathologic features may be indistinguishable from those of the central giant cell granuloma.10 The condition characteristically presents itself in children between 2 to 4 years of age and is manifested by painless, bilateral enlargement of the mandible, occasionally accompanied by involvement of the maxilla. If the disease process extends into the infraorbital region, the inferior portion of the sclera appears more
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