Case Report
Myocardial fibrosis in desmin-related hypertrophic cardiomyopathy

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Abstract

Desmin-related myopathy (DRM) is known to cause different types of cardiomyopathy. Late gadolinium enhancement cardiovascular magnetic resonance (CMR) has been shown to identify fibrosis in ischemic and non-ischemic cardiomyopathies. We present a rare case of desmin-related hypertrophic cardiomyopathy, CMR revealed fibrosis in the lateral wall of the left ventricle. CMR is superior to conventional echocardiography for the detection of myocardial fibrosis in desmin-related cardiomyopathy, which may be useful to detect early cardiac involvement and predict the patient prognosis.

Keywords

Cardiomyopathy
Cardiovascular Magnetic Resonance
Late Gadolinium Enhancement
Brain Natriuretic Peptide
Myocardial Fibrosis

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